There are several different types of Usher syndrome. These are caused by different genes.
Usher Type 1
People with Type 1 are profoundly deaf from birth, with poor balance. The progressive eye condition, Retinitis Pigmentosa (RP for short) can be noticeable before the age of 10
Usher Type 2
People with Type 2 have a partial to severe hearing loss from birth. Their balance is normal. The RP is usually, but not always, noticeable before the age of 20
Usher Type 3
This is the rarest type of Usher in the UK. People with Type 3 have normal sight and either normal or partial hearing at birth. The deterioration of the hearing and the diagnosis of the RP commonly happen at roughly the same time, either in adulthood or, occasionally, in children or teenagers. Balance can become affected over time
